Protein Information

Name phenylalanine hydroxylase
Synonyms PAH; PKU; PKU 1; PKU1; Phe 4 monooxygenase; Phenylalanine hydroxylase; Phenylalanine 4 hydroxylase; PAH…

Compound Information

Name IAA
CAS

Reference List

PubMed Abstract RScore(About this table)
11382545 Keene JC, Austic RE: Dietary supplements of mixtures of indispensable amino acids lacking threonine, phenylalanine or histidine increase the activity of hepatic threonine dehydrogenase, phenylalanine hydroxylase or histidase, respectively, and prevent growth depressions in chicks caused by dietary excesses of threonine, phenylalanine, or histidine*. J Nutr Biochem. 2001 May;12(5):274-284.

2(0,0,0,2) Details
18212372 Lartey FM, Austic RE: Phenylalanine requirement, imbalance, and dietary excess in one-week-old chicks: growth and phenylalanine hydroxylase activity. Poult Sci. 2008 Feb;87(2):291-7.

1(0,0,0,1) Details
18203898 Ney DM, Hull AK, van Calcar SC, Liu X, Etzel MR: Dietary glycomacropeptide supports growth and reduces the concentrations of phenylalanine in plasma and brain in a murine model of phenylketonuria. J Nutr. 2008 Feb;138(2):316-22.


Phenylketonuria (PKU) is a genetic disorder caused by deficiency of phenylalanine hydroxylase (PAH) that requires life-long adherence to a low-phenylalanine (Phe) diet.
1(0,0,0,1) Details
19276420 Lartey FM, Austic RE: Phenylalanine hydroxylase activity and expression in chicks subjected to phenylalanine imbalance or phenylalanine toxicity. Poult Sci. 2009 Apr;88(4):774-83.

1(0,0,0,1) Details