Protein Information

Name DORV
Synonyms Brachyury; CAFS; CTHM; DGCR; DGS; DORV; T box 1; T box 1 transcription factor C…

Compound Information

Name IAA
CAS

Reference List

PubMed Abstract RScore(About this table)
19555560 Zhang HL, Li SJ, Hu SS, Liu YL, Shen XD, Yan J: [Results of surgical treatment of 1,387 infants under 6 months of age with congenital heart disease]. Zhonghua Er Ke Za Zhi. 2009 Apr;47(4):250-4.


There were 675 cases with ventricular septal defect with pulmonary hypertension (VSD/PH), 138 with complete transposition of the great arteries (TGA), 155 with tetralogy of Fallot (TOF), 111 with totally abnormal pulmonary venous connection (TAPVC), 54 with coarctation of aorta or interrupted aortic arch with ventricular septal defect [CoA (IAA)/VSD], 46 with double outlet right ventricle (DORV), 25 with pulmonary atresia with ventricular septal defect (PA/VSD), 24 with pulmonary atresia with intact interventricular septum (PA/IVS) and so on.
1(0,0,0,1) Details
12238838 Allen BS, El-Zein C, Cuneo B, Cava JP, Barth MJ, Ilbawi MN: Pericardial tissue valves and Gore-Tex conduits as an alternative for right ventricular outflow tract replacement in children. Ann Thorac Surg. 2002 Sep;74(3):771-7.


Diagnosis included tetralogy of Fallot (n = 25); truncus arteriosis (n = 9); ventricular septal defect with PA (n = 5); DORV (n = 4); D-TGA with PS (n = 2); and 1 each IAA with sub AS, VSD with PI, and PS s/p Ross procedure.
1(0,0,0,1) Details
16132309 Khositseth A, Tocharoentanaphol C, Khowsathit P, Ruangdaraganon N: Chromosome 22q11 deletions in patients with conotruncal heart defects. Pediatr Cardiol. 2005 Sep-Oct;26(5):570-3.


Sixty-one patients with conotruncal heart defects, including tetralogy of Fallot (TOF; n = 32), pulmonary atresia/ventricular septal defect (PAVSD; n = 12), double-outlet right ventricle (DORV; n = 5), transposition of the great arteries (TGA; n = 4 ), truncus arteriosus (TA; n = 4), subpulmonary ventricular septal defect (SPVSD; n = 3), and interrupted aortic arch (IAA; n = 1), were enrolled in this study and screened for 22q11 deletions by the fluorescence in situ hybridization technique.
1(0,0,0,1) Details
10967928 Malec E, Werynski P, Mroczek T, Mikuta M, Kolcz J, Januszewska K, Pajak J: [Results of surgical treatment of congenital heart defects in infants below 2500 grams]. Przegl Lek. 2000;57(4):187-90.


Cardiac diagnoses included patent ductus arteriosus (PDA) (N = 21, 28.7%), ventricular septal defect (VSD) (N = 9, 12.3%), transposition of great arteries (TGA) (N = 10, 13.7%), tetralogy of Fallot (TOF) (N = 7, 9.6%), double-outlet right ventricle (DORV) (N = 4, 5.5%), truncus arteriosus communis (TAC) (N = 4, 5.5%), hypoplastic left heart syndrome (HLHS) (N = 4, 5.5%), coarctation of aorta (CoAo) (N = 6, 8.2%), total anomalous pulmonary venous return (TAPVR) (N = 2, 2.7%), aortic stenosis (AoVS) (N = 3, 4.1%), interrupted aortic arch (IAA) (N = 1, 1.4%), pulmonary atresia (PA) (N = 1, 1.4%) and common atrioventricular canal (CAVC) (N = 1, 1.4%).
1(0,0,0,1) Details
12632898 Moll JA, Binikowska J, Ostrowska K, Makowiecka E, Sysa A, Moll JJ: [The role of transesophageal echocardiography (TEE) in assessment of left ventricular tract obstruction]. Przegl Lek. 2002;59(9):732-6.


Nine of them developed left ventricular outflow obstruction after surgery for congenital heart disease (VSD + IAA, VSD + DORV, VSD + TGA, VSD + CoA) and then developed an isolated form of primary stenosis.
1(0,0,0,1) Details
12956042 Kopf GS, Mello DM: Surgery for congenital heart disease in low-birth weight neonates: a comprehensive statewide Connecticut program to improve outcomes. Conn Med. 2003 Jun-Jul;67(6):327-32.


Primary diagnoses included variant of single ventricle (8), ventricular septal defect (VSD) (4), tetralogy of Fallot (TOF) (2), pulmonary atresia (PA) with VSD (3), simple transposition of the great arteries (TGA) (1), TGA with VSD (TGA/VSD) (2), atrioventricular canal (AVC) (4), double outlet right ventricle (DORV) (3), aortic coarctation (CoA) (2), and interrupted aortic arch with VSD (IAA/VSD) (3).
1(0,0,0,1) Details
16824627 Park IS, Ko JK, Kim YH, Yoo HW, Seo EJ, Choi JY, Gil HY, Kim SJ: Cardiovascular anomalies in patients with chromosome 22q11.2 deletion: a Korean multicenter study. Int J Cardiol. 2007 Jan 8;114(2):230-5. Epub 2006 Jul 7.


RESULTS: A total of 222 patients were examined and 190 (85.6%) patients had the cardiovascular abnormalities: 63.2% tetralogy of Fallot (TOF), 20.5% isolated ventricular septal defects (VSDs), 5.3% interrupted aortic arch type B (IAA B), 3.6% double outlet right ventricle (DORV), 3.6% atrial septal defects (ASDs) and 1.7% truncus arteriosus (TA).
1(0,0,0,1) Details