Protein Information

Name 2 methyl 3 hydroxybutyryl CoA dehydrogenase
Synonyms 17b HSD10; SCHAD; 17beta hydroxysteroid dehydrogenase type 10; 2 Methyl 3 hydroxybutyryl CoA dehydrogenase; 2 Methyl 3 hydroxybutyryl Coenzyme A dehydrogenase; 3 hydroxy 2 methylbutyryl CoA dehydrogenase; 3 hydroxy 2 methylbutyryl Coenzyme A dehydrogenase; 3 hydroxyacyl CoA dehydrogenase type II…

Compound Information

Name MAA
CAS methylarsonic acid

Reference List

PubMed Abstract RScore(About this table)
15902553 Rosa RB, Schuck PF, de Assis DR, Latini A, Dalcin KB, Ribeiro CA, da C Ferreira G, Maria RC, Leipnitz G, Perry ML, Filho CS, Wyse AT, Wannmacher CM, Wajner M: Inhibition of energy metabolism by 2-methylacetoacetate and 2-methyl-3-hydroxybutyrate in cerebral cortex of developing rats. J Inherit Metab Dis. 2005;28(4):501-15.


Mitochondrial beta-ketothiolase and 2-methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiencies are inherited neurometabolic disorders affecting isoleucine catabolism.		 5(0,0,0,5) Details